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IJBC 2017, 9(4): 128-129 Back to browse issues page
A Rare Case of Co-Inheritance of Beta Thalassemia Intermedia and Coagulation FVII Deficiency
Zahra Barati Shourijeh , Mehran Karimi *
Hematology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Abstract:   (808 Views)

We present a 34-year-old man with combination of beta thalassemia intermedia and coagulation factor VII deficiency who was presented with pallor and irregular nose bleeding episodes. On physical examination, he had splenomegaly and yellow sclera. Pallor and splenomegaly could be reminder of thalassemic syndromes or hemoglobinopathies including thalassemia intermedia. Association with unusual bleeding tendency such as prolonged and repeated episodes of epistaxis without any evidence of liver failure in hemoglobinopathies suggest the possibility of coinheritance of a bleeding disorder. As a result, coagulation assay for proper diagnosis, management and prevention of probable life-threatening bleeding episodes is suggested. 

Keywords: Thalassemia intermedia, Factor VII deficiency, Coinheritance, Liver failure, Hypercoagulability, Bleeding tendency
Full-Text [PDF 388 kb]   (391 Downloads)    
: case report | Subject: Adults Hematology & Oncology
Received: 2017/05/22 | Accepted: 2017/10/8 | Published: 2018/03/4
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Barati Shourijeh Z, Karimi M. A Rare Case of Co-Inheritance of Beta Thalassemia Intermedia and Coagulation FVII Deficiency. IJBC. 2017; 9 (4) :128-129
URL: http://ijbc.ir/article-1-731-en.html

Volume 9, Issue 4 (December 2017 2017) Back to browse issues page
مجله ی خون و سرطان ایران Iranian Journal of Blood and Cancer
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