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Volume 16, Issue 3 (September 2024 2024)
Iranian Journal of Blood and Cancer 2024, 16(3): 8-13 |
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Tabatabaii S A, Entezari Farahabadi N. Management of Hypoxia in the Simultaneous Presentation of Sickle Cell Trait and Cystic Fibrosis. Exploring a Rare Case with a Comprehensive Review. Iranian Journal of Blood and Cancer 2024; 16 (3) :8-13
URL: http://ijbc.ir/article-1-1606-en.html
URL: http://ijbc.ir/article-1-1606-en.html
1- Department of Pediatric Pulmonology, Mofid Pediatrics Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran
2- Department of Pediatric Pulmonology, Mofid Pediatrics Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran ,neda93farahabadi@gmail.com
2- Department of Pediatric Pulmonology, Mofid Pediatrics Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran ,
Abstract: (143 Views)
Background: Cystic fibrosis (CF) is an inheriting disorder that has a strong impact on the pulmonary systems of individuals, as a result, hypoxia might be presented among patients who have CF. In addition, hypoxia is a pathological condition that might be present among patients with sickle cell trait (SCT). However, the simultaneous presentation of both SCT and CF in a patient is rare.
Case presentation: A 7-year-old boy came to the hospital with a chief complaint of cyanosis and cough. In his physical examination, he has low SpO2. His fiber-optic bronchoscopy depicted purulent secretion in the main bronchus. As well, his sweet chloride test was above 80 mmol/L. Thus, by the impression of CF exacerbation, he got HARD treatment and antibiotics. Additionally, during hospitalization, SCT as another impression was diagnosed for him.
Conclusion: Although the co-existence of CF and SCT is rare among patients. The physicians must consider both CF and SCT when a child comes to the emergency room with hypoxia.
Case presentation: A 7-year-old boy came to the hospital with a chief complaint of cyanosis and cough. In his physical examination, he has low SpO2. His fiber-optic bronchoscopy depicted purulent secretion in the main bronchus. As well, his sweet chloride test was above 80 mmol/L. Thus, by the impression of CF exacerbation, he got HARD treatment and antibiotics. Additionally, during hospitalization, SCT as another impression was diagnosed for him.
Conclusion: Although the co-existence of CF and SCT is rare among patients. The physicians must consider both CF and SCT when a child comes to the emergency room with hypoxia.
: Case report |
Subject:
Pediatric Hematology & Oncology
Received: 2024/08/13 | Accepted: 2024/09/23 | Published: 2024/09/30
Received: 2024/08/13 | Accepted: 2024/09/23 | Published: 2024/09/30
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