Chetak K, Hiremath V, Sujay K R, Dinesh Kumar U S, Jagadish kumar K. Congenital Hypofibrinogenemia Detected during Preoperative Workup for Major Cardiac Surgery. Iranian Journal of Blood and Cancer 2018; 10 (3) :96-98
URL:
http://ijbc.ir/article-1-808-en.html
1- , jagdishmandya@gmail.com
Abstract: (3915 Views)
Afibrinogenemia or hypofibrinogenemia is a quantitative defect in fibrinogen. It is a rare disease with estimated frequency of 1 in 1,000,000 population. Routine preoperative screening tests of coagulation disorders are insufficient to detect subtle disorders of fibrinogen. Herein, we report a child who was supposed to undergo open cardiac surgery for a large atrial septal defect. Preoperative coagulation screening tests revealed minimal prolongation of prothrombin time which made us do further work-up. Finally, she was diagnosed with hypofibrinogenemia who was suggested to be congenital.
:
Case report |
Subject:
Pediatric Hematology & Oncology Received: 2018/06/7 | Accepted: 2018/08/26 | Published: 2018/10/24