Kaposiform Hemangioendothelioma of Abdominal Wall Associated with Kasabach-Merritt in A Newborn with Dramatic Response to Sirolimus and Vincristine

Alavi, Samin

doi:10.58209/ijbc.14.1.46

Volume 14, Issue 1 ( March 2022 2022) Iranian Journal of Blood and Cancer 2022, 14(1): 46-48 | Back to browse issues page

‎ 10.58209/ijbc.14.1.46

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Alavi S. Kaposiform Hemangioendothelioma of Abdominal Wall Associated with Kasabach-Merritt in A Newborn with Dramatic Response to Sirolimus and Vincristine. Iranian Journal of Blood and Cancer 2022; 14 (1) :46-48
URL: http://ijbc.ir/article-1-1249-en.html

Kaposiform Hemangioendothelioma of Abdominal Wall Associated with Kasabach-Merritt in A Newborn with Dramatic Response to Sirolimus and Vincristine

Samin Alavi ^*

Pediatric Congenital Hematologic Disorders Research Center, Research Institute for Children’s health, Shahid Beheshti University of Medical Sciences, Tehran, Iran.

Abstract: (1875 Views)

Kaposiform Hemangioendotheliomawas (KHE) first described in 1993 by Zukerberg and colleagues as a distinctive lesion of infancy and early childhood with common features to both hemangiomas and Kaposi’s sarcoma. It is a rare vascular tumor typically seen as a cutaneous lesion with ill-defined borders. In this study we presented A 26-day-old male infant with KHE.

Keywords: Kaposiform Hemangioendothelioma, Kasabach-Merritt, Vincristine, Sirolimus.

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: Special Issue | Subject: Adults Hematology & Oncology
Received: 2022/04/30 | Accepted: 2022/03/10 | Published: 2022/04/30

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